RETROPERITONEAL CYSTIC LYMPHANGIOMA: CASE REPORT OF A RARE ENTITY

  • Isabel Vieira Serviço de Angiologia e Cirurgia Vascular — Hospital do Divino Espírito Santo de Ponta Delgada, Portugal
  • Emanuel Dias Serviço de Angiologia e Cirurgia Vascular — Hospital do Divino Espírito Santo de Ponta Delgada, Portugal
  • Lisa Borges Serviço de Angiologia e Cirurgia Vascular — Hospital do Divino Espírito Santo de Ponta Delgada, Portugal
  • Alberto Henrique Serviço de Angiologia e Cirurgia Vascular — Hospital do Divino Espírito Santo de Ponta Delgada, Portugal
  • Nelson Oliveira Serviço de Angiologia e Cirurgia Vascular — Hospital do Divino Espírito Santo de Ponta Delgada, Portugal
  • Isabel Cássio Serviço de Angiologia e Cirurgia Vascular — Hospital do Divino Espírito Santo de Ponta Delgada, Portugal
Keywords: Cystic lymphangioma, Retroperitoneum, Cystic abdominal mass, Surgical excision

Abstract

Cystic lymphangioma is a rare and benign malformation of the lymphatic system, with retroperitoneal location accounting for only 1% of all lymphangiomas. Clinical presentation is frequently nonspecific. Authors present a case report of a 38 years old woman with persistent abdominal pain refractory to treatment that required imaging investigation (abdominal ultrasound and thoraco-abdominopelvic computed tomography scan) unveiling a cystic retroperitoneal mass suggesting lymphangioma. Abdominal laparotomy was performed for complete excision of the tumor. Histopathological exam of surgical specimen confirmed the cystic lymphangioma diagnosis. Complete surgical excision is considered gold-standard therapy and allow definite diagnosis.

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Published
2021-06-03
Section
Clinical Case