RETROPERITONEAL CYSTIC LYMPHANGIOMA: CASE REPORT OF A RARE ENTITY

Authors

  • Isabel Vieira Serviço de Angiologia e Cirurgia Vascular — Hospital do Divino Espírito Santo de Ponta Delgada, Portugal
  • Emanuel Dias Serviço de Angiologia e Cirurgia Vascular — Hospital do Divino Espírito Santo de Ponta Delgada, Portugal
  • Lisa Borges Serviço de Angiologia e Cirurgia Vascular — Hospital do Divino Espírito Santo de Ponta Delgada, Portugal
  • Alberto Henrique Serviço de Angiologia e Cirurgia Vascular — Hospital do Divino Espírito Santo de Ponta Delgada, Portugal
  • Nelson Oliveira Serviço de Angiologia e Cirurgia Vascular — Hospital do Divino Espírito Santo de Ponta Delgada, Portugal
  • Isabel Cássio Serviço de Angiologia e Cirurgia Vascular — Hospital do Divino Espírito Santo de Ponta Delgada, Portugal

DOI:

https://doi.org/10.48750/acv.380

Keywords:

Cystic lymphangioma, Retroperitoneum, Cystic abdominal mass, Surgical excision

Abstract

Cystic lymphangioma is a rare and benign malformation of the lymphatic system, with retroperitoneal location accounting for only 1% of all lymphangiomas. Clinical presentation is frequently nonspecific. Authors present a case report of a 38 years old woman with persistent abdominal pain refractory to treatment that required imaging investigation (abdominal ultrasound and thoraco-abdominopelvic computed tomography scan) unveiling a cystic retroperitoneal mass suggesting lymphangioma. Abdominal laparotomy was performed for complete excision of the tumor. Histopathological exam of surgical specimen confirmed the cystic lymphangioma diagnosis. Complete surgical excision is considered gold-standard therapy and allow definite diagnosis.

Downloads

Download data is not yet available.

References

1. Bhavsar T, Saeed-Vafa D, Harbison S, et al. Retroperitoneal cystic lymphangioma an an adult: a case report and review of the literature. World J Gastrointest Pathophysiol. 2010;1(5):171–6.

2. Chung SH, Park YS, JO YJ, et al. Asymptomatic lymphangioma involving the spleen and retroperitoneum in adults. World J Gastroenterol. 2009;15(44):5620–3.

3. Mabrouk MB, Barka M, Farhat W, et al. Intra-abdominal cystic lymphangioma: Report of 21 cases. J Cancer Therapy. 2015;6:572–8.

4. Yang DM, Jung DH, Kim H, et al. Retroperitoneal cystic masses: CT, clinical, and pathologic findings and literature review. Radiographics. 2004;24(5):1353–65.

5. Perrot M, Rostan O, Morel P, et al. Abdominal lymphangioma in adults and children. Br J Surg. 1998;85(3)395–7.

6. Cherk M, Nikfarjam M, Christophi C, et al. Retroperitoneal lymphangioma. Asian J Surg, 2006;29(1):51–4.

7. Surlin V, Georgescu E, Dumitrescu C, et al. Retropancreatic cystic lymphangioma – considerations upon a case. Rom J Morphol Embryol. 2011;52(1):493–6.

8. Chew BJW, Dagash H, Khare MM. Intra-Abdominal Cystic Lymphangioma. J Pediatr; 2019;205:288-288.

9. Wilson SR, Boher S, Losada R, et al. Retroperitoneal lymphangioma: an unusual location and presentation. J Ped Surg. 2006;41(3):601–5.

10. Rani DV, Srilakshmi R, Malathi S, et al. Unusual presentation of a retroperitoneal lymphangioma. 2006; 73(7):617-8.

11. Nijjar I, Singh JP, Arova V, et al. Retroperitoneal cystic lymphangiom. Ind J Radiol Imag. 2004;14(4):413–4.

12. Tripathi M, Parshad S, Karwasra RK, et al. Retroperitoneal lymphangioma in an adult: a case report of a rare clinical entity. 2015;ID 732531:1-4.

13. Hauser H, Mischinger HJ, Beham A, et al. Cystic retroperitoneal lymphangiomas in adults. Eur J Surg Oncol. 1997;23:322–6.

14. Nuzzo G, Lemmo G, Marrocco-Trischitta MM, et al. Retroperitoneal cystic lymphangioma. J Surg Oncol. 1996;61:234–7.

15. Kasza J, Brody FJ, Khambaty F, et al. Laparoscopic resection of a retroperitoneal cystic lymphangioma in an adult. 2010;20(3):114–6.

16. Casadei R, Minni F, Selva S, et al. Cystic lymphangioma of the pancreas: anatomoclinical, diagnostic and therapeutic considerations regarding three personal observations and review of the literature. Hepatogastroenterology. 2003;50(53):1681-6.

17. Xv FY, Sun A, Gan Y, et al. Gastric duplication cyst mimicking large cystic lymphangioma in an adult: A rare case report and review of the literature. World J Clin Cases 2019; 7(15):2087-2093.

Published

2021-06-03

How to Cite

1.
Vieira I, Dias E, Borges L, Henrique A, Oliveira N, Cássio I. RETROPERITONEAL CYSTIC LYMPHANGIOMA: CASE REPORT OF A RARE ENTITY. Angiol Cir Vasc [Internet]. 2021 Jun. 3 [cited 2024 Apr. 19];17(1):43-6. Available from: https://acvjournal.com/index.php/acv/article/view/380

Issue

Section

Clinical Case